Generic name:nitisinone [ nye-TIS-i-none ]
Drug class:Miscellaneous metabolic agents
Medically reviewed by Drugs.com. Last updated on Apr 9, 2021.
What is Nityr?
Nityr is a hydroxyphenyl-pyruvate dioxygenase inhibitor.
Nityr is used to treat adult and children with a rare genetic condition called hereditary tyrosinemia type 1 (HT-1) along with with dietary restriction of tyrosine and phenylalanine. HT-1 is a metabolic disorder that occurs when the body does not produce enough of an enzyme that breaks down proteins from certain foods. This condition occurs most often in young babies.
Nityr works by preventing the body from breaking down an amino acid called tyrosine and by keeping other toxic substances from building up and causing harm to your liver or kidneys.
Warnings
Call your doctor at once if you have vision problems, eye pain, eye redness or burning, easy bruising, unusual bleeding, itching, or jaundice (yellowing of the skin or eyes). Tell your doctor if your baby has a sudden change in behavior, ability, or development (sitting up, crawling, walking, talking, etc).
Before taking this medicine
Tell your doctor if you have any medical conditions affecting your eyes.
Tell your doctor if you are pregnant or breastfeeding.
How should I take Nityr?
Take Nityr exactly as directed. Follow all directions on your prescription label and read all medication guides or instruction sheets. Your doctor may occasionally change your dose.
Do not change your medication dose or schedule without your doctor's advice.
You must avoid certain foods for your treatment to be effective. Follow the diet plan created for you by your doctor or nutrition counselor.
High protein foods are high in tyrosine and phenylalanine (including artificial sweeteners such as aspartame, Equal, or Nutrasweet). Since babies and children need...
