Procysbi
Generic name:cysteamine [ sis-TEE-a-meen ]
Brand names: Cystagon, Procysbi
Drug class:Miscellaneous uncategorized agents
What is Procysbi?
Procysbi works by reducing the amount of cystine (an amino acid) in the body.
Procysbi is used to treat nephropathic cystinosis (NEF-roe-PATH-ik SIS-tin-OH-sis), a rare genetic condition that causes a build-up of cystine in the kidneys and other organs. Too much cystine can cause kidney failure or other medical problems.
Procysbi is for use in adults and children, but Procysbi should not be given to a child younger than 1 year old.
Warnings
Follow all directions on your medicine label and package. Tell each of your healthcare providers about all your medical conditions, allergies, and all medicines you use.
Before taking this medicine
You should not use Procysbi if you are allergic to cysteamine or penicillamine.
To make sure Procysbi is safe for you, tell your doctor if you have:
any type of skin rash;
bone problems (including fractures);
epilepsy or other seizure disorder;
low white blood cell (WBC) counts;
depression, drowsiness, or nervous system disorder; or
stomach ulcer, or bleeding in your stomach or intestines.
It is not known whether cysteamine will harm an unborn baby. Tell your doctor if you are pregnant or plan to become pregnant.
You should not breastfeed while using Procysbi.
How should I use Procysbi?
Take Procysbi exactly as prescribed by your doctor. Follow all directions on your prescription label and read all medication guides or instruction sheets. Your doctor may occasionally change your dose.
Take Procysbi with water or fruit juice, but not grapefruit juice. You may take Procysbi with or without food, but take it the same way each time.
To take Procysbi with food, eat only a small amount (1/2 cup) of food within 1 hour before or 1 hour after you take the medicine.
To take Procysbi without food, take the medicine at least 30 minutes before or 2 hours after a meal.
Swallow the capsule whole and do not crush or chew it.
If you cannot swallow a capsule whole, carefully follow the patient instructions for opening the capsule and mixing the medicine with certain foods. Your doctor may recommend that you use cysteamine oral granules.
Do not crush or chew oral granules.
Procysbi works best if you take it without food, at least 30 minutes before or 2 hours after a meal. If you cann...